Known for his work on such acclaimed Danish films as Dogville, Melancholia, and Dancer in the Dark, he also produced the Academy Award-nominated movie After the Wedding. In the 1990s, he earned a reputation as the top film producer in Denmark.
In the early 1990s, he and director Lars von Trier established a Danish movie production house called Zentropa.
Icelandic pop singer Björk starred in his 2000 film Dancer in the Dark.
He married Lise Palm in September of 1983.
Actress Nicole Kidman was the star of his 2003 film Dogville.